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Maple Syrup Urine Disease

Reviewed by the medical team of El Doctor Editorial policy

Maple syrup urine disease is an inherited metabolic disorder in which the body does not properly process certain amino acids, causing them to build up and producing a characteristic sweet smell in the urine.

Signs in the baby:

  • A peculiar urine odor, similar to maple syrup.
  • Feeding difficulties, vomiting, or excessive sleepiness.
  • Irritability or changes in muscle tone.

Why is early detection important? It is a condition present from birth, so identifying it early is essential for the child's care.

Who evaluates it? The pediatrician performs the initial evaluation and, when it is suspected, refers to specialists in metabolic diseases. If a newborn shows these signs, it is essential to seek medical attention immediately.

Data on 17 doctors who treat maple syrup urine disease

Typical price
$800 MXN
33% above the national median
50% charge between $650 and $1,000 MXN
100% with verified license

Which specialist treats maple syrup urine disease?

Maple Syrup Urine Disease is usually treated by specialists in pediatrician, pediatric surgeon, infectious disease specialist, general practitioner, pediatric nephrologist, pediatric urologist.

Treatment by city

Doctors specialized in maple syrup urine disease

Dr. Rodrigo Armando Vigueras Santiago

Dr. Rodrigo Armando Vigueras Santiago

General Practitioner
5.0 (4 reviews)
Clinica Delicias
Prices from
$250 MXN
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Dr. Vicente de Jesus Flores Lopez

Dr. Vicente de Jesus Flores Lopez

General Practitioner
2 reviews
Deposito Dental
Prices from
$1,000 MXN
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Dr. Jacqueline Montero Schwarz

Dr. Jacqueline Montero Schwarz

General Practitioner
5.0 (3 reviews)
PLAYA DEL CARMEN - "Clínica FisioPlaya"
Prices from
$700 MXN
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LV

Dr. Lorely Vianey Bres Ramírez

Pediatrician
1 review
Consulta pediátrica
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Dr. Maria Fernanda Frausto Mendoza

Dr. Maria Fernanda Frausto Mendoza

General Practitioner · Clinical Nutritionist
5.0 (3 reviews)
Instituto Bioprogresivo DE Ortodoncia
Prices from
$250 MXN
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Dr. Karla Escobedo Vázquez

Dr. Karla Escobedo Vázquez

General Practitioner
5.0 (4 reviews)
DermoPerfection- Medical Spa.
Prices from
$700 MXN
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Dr. Norma Ilse Garcia González

Dr. Norma Ilse Garcia González

General Practitioner
5.0 (10 reviews)
MERR CLINICS
Prices from
$800 MXN
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Dr. Kim Danae Díaz Juárez

Dr. Kim Danae Díaz Juárez

Pediatrician
5.0 (10 reviews)
Farmacia Santa Anita
Prices from
$900 MXN
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Dr. Carlos Andrés Aceves Barrios

Dr. Carlos Andrés Aceves Barrios

Pediatrician
5.0 (10 reviews)
MedHaus Coyoacán Consultorio C-106,
Prices from
$1,000 MXN
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Dr. Héctor Garza Blizzard

Dr. Héctor Garza Blizzard

General Practitioner
5.0 (10 reviews)
Farmacia Central Homeopatica
Prices from
$900 MXN
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Dr. Gilberto Morales Salgado

Dr. Gilberto Morales Salgado

General Practitioner
1 review
Farmacia EL Botiquin
Prices from
$450 MXN
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Dr. Stephany Sbheidy García Arana

Dr. Stephany Sbheidy García Arana

Pediatric Nephrologist
5.0 (9 reviews)
Optica Vez EL Mejor Punto DE Vista
Prices from
$500 MXN
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Dr. Miguel Ángel Martínez Benaiges

Dr. Miguel Ángel Martínez Benaiges

Pediatrician
5.0 (10 reviews)
Denta Alex
Prices from
$800 MXN
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GF

Dr. Guillermo Fojaco Villanueva

Pediatrician
5.0 (10 reviews)
Hector Jose Castro Macias
Prices from
$1,500 MXN
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Dr. Ivette Victorino

Dr. Ivette Victorino

Pediatrician
5.0 (10 reviews)
Medicina, Belleza y Salud
Prices from
$1,100 MXN
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Dr. Oscar Yair Nava Garcia

Dr. Oscar Yair Nava Garcia

General Practitioner
1 review
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Dr. Sandra Herrera Rodriguez

Dr. Sandra Herrera Rodriguez

Pediatrician
5.0 (10 reviews)
Administracion Torre Medica Nueva York 32
Prices from
$500 MXN
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Dr. Valeria Gómez Galván

Dr. Valeria Gómez Galván

Pediatrician
5.0 (10 reviews)
Administracion Torre Medica Nueva York 32
Prices from
$900 MXN
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Dr. Andrea Piñeyro V.

Dr. Andrea Piñeyro V.

Pediatrician
5.0 (10 reviews)
Administracion Torre Medica Nueva York 32
Prices from
$500 MXN
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Dr. Elisa Barrios Santos

Dr. Elisa Barrios Santos

Pediatrician
5.0 (10 reviews)
Town Center
Prices from
$700 MXN
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Frequently asked questions

What is maple syrup urine disease?

Maple syrup urine disease is an inherited metabolic disorder in which the body does not properly process certain amino acids, causing them to build up and producing a characteristic sweet smell in the urine.

Which doctor treats maple syrup urine disease?

Maple Syrup Urine Disease is usually treated by specialists in pediatrician, pediatric surgeon, infectious disease specialist, general practitioner, pediatric nephrologist, pediatric urologist.